ICD-10 D81.819
Billable / SpecificBiotin-dependent carboxylase deficiency, unspecified
About ICD-10-CM D81.819
ICD-10-CM code D81.819 represents Biotin-dependent carboxylase deficiency, unspecified. This is a billable/specific code in the Blood and Blood-forming Organs chapter (block D81). The 2026 edition of ICD-10-CM D81.819 became effective on October 1, 2025.
Inclusion Terms / Approximate Synonyms
Clinical terms and conditions classified under D81.819. Per CMS ICD-10-CM Tabular 2026.
- Multiple carboxylase deficiency, unspecified
Medicare LCD Coverage for D81.819
Local Coverage Determinations (LCDs) from CMS MACs that list D81.819 as a covered diagnosis.
Showing top 10 of 29 total . Click a CPT for full coverage scope.
Commercial Payer Coverage
Coverage policies from major commercial payers referencing D81.819.
5 Medicare
1 Aetna
Convert D81.819 to ICD-9-CM
Per CMS General Equivalence Mappings (GEMs), useful for legacy data review and historical claim analysis.
| ICD-10 | ICD-9 | Mapping Flags |
|---|---|---|
| D81.819 | 2662 | 10000 |
Flags format (5 digits): Approximate · No Map · Combination · Scenario · Choice List. Source: CMS 2017 GEMs (final version).
Codes Adjacent To D81.819
Other codes in section D80-D89 (Certain disorders involving the immune mechanism).
ICD-10 D81.819, Billing FAQ
Is ICD-10 code D81.819 billable? +
Yes, D81.819 is a billable ICD-10-CM code that can appear as a primary or secondary diagnosis on claims.
What other names or terms map to D81.819? +
ICD-10 D81.819 includes: Multiple carboxylase deficiency, unspecified.
What CPT codes are commonly billed with D81.819? +
Procedures frequently paired with D81.819 include: J3420, J3425.
What ICD-9 codes does D81.819 map to? +
Per CMS GEMs, D81.819 maps to ICD-9 codes: 2662. Useful for legacy data review and historical claim analysis.
Get the full PayerReady toolkit
Free access to CPT/ICD-10 lookup, denial appeals, fee comparator, and claim auditing with credentialing enrollment.
Start free →Run this code through our claim audit tool
Check NCCI bundling, MUE limits, and modifier logic before submission.
Try the auditor →Did this page help?
Quick signal so we know what to improve.
If you want a code reference page that doesn't exist yet, email coding@payerready.com.
Tell us what's missing or wrong: coding@payerready.com. We respond within 5 business days.
Reviewed by the PayerReady Medical Coding Team
Verified against the CMS 2026 code set on June 1, 2026.
Powered by 11K CPT · 98K ICD-10 · 860K MPFS rates · 4.5M NCCI edits · 9.5M NPIs. Our data methodology · About our coding team