Pulmonary heart disease and diseases of pulmonary circulation
41 codes in this section
About Section I26-I28
Section I26-I28 (I26-I28) covers pulmonary heart disease and diseases of pulmonary circulation. It sits within the Diseases of the circulatory system chapter (I00-I99). This section contains 41 ICD-10-CM codes, 33 billable diagnoses you can submit on a claim, and 8 non-billable header codes used to organize the hierarchy.
Codes are organized below by 3-character root. Click the root to see all subcodes underneath it, or click any individual code for full coverage data, payer policies, and linked CPT procedures.
Codes in I26-I28
Grouped by 3-character root code. Click any code for full detail.
| I26.0 | Pulmonary embolism with acute cor pulmonale | Header |
| I26.01 | Septic pulmonary embolism with acute cor pulmonale | Billable |
| I26.02 | Saddle embolus of pulmonary artery with acute cor pulmonale | Billable |
| I26.03 | Cement embolism of pulmonary artery with acute cor pulmonale | Billable |
| I26.04 | Fat embolism of pulmonary artery with acute cor pulmonale | Billable |
| I26.09 | Other pulmonary embolism with acute cor pulmonale | Billable |
| I26.9 | Pulmonary embolism without acute cor pulmonale | Header |
| I26.90 | Septic pulmonary embolism without acute cor pulmonale | Billable |
| I26.92 | Saddle embolus of pulmonary artery without acute cor pulmonale | Billable |
| I26.93 | Single subsegmental thrombotic pulmonary embolism without acute cor pulmonale | Billable |
| I26.94 | Multiple subsegmental thrombotic pulmonary emboli without acute cor pulmonale | Billable |
| I26.95 | Cement embolism of pulmonary artery without acute cor pulmonale | Billable |
| I26.96 | Fat embolism of pulmonary artery without acute cor pulmonale | Billable |
| I26.99 | Other pulmonary embolism without acute cor pulmonale | Billable |
| I27.0 | Primary pulmonary hypertension | Billable |
| I27.1 | Kyphoscoliotic heart disease | Billable |
| I27.2 | Other secondary pulmonary hypertension | Header |
| I27.20 | Pulmonary hypertension, unspecified | Billable |
| I27.21 | Secondary pulmonary arterial hypertension | Billable |
| I27.22 | Pulmonary hypertension due to left heart disease | Billable |
| I27.23 | Pulmonary hypertension due to lung diseases and hypoxia | Billable |
| I27.24 | Chronic thromboembolic pulmonary hypertension | Billable |
| I27.29 | Other secondary pulmonary hypertension | Billable |
| I27.8 | Other specified pulmonary heart diseases | Header |
| I27.81 | Cor pulmonale (chronic) | Billable |
| I27.82 | Chronic pulmonary embolism | Billable |
| I27.83 | Eisenmenger's syndrome | Billable |
| I27.84 | Fontan related circulation | Header |
| I27.840 | Fontan-associated liver disease [FALD] | Billable |
| I27.841 | Fontan-associated lymphatic dysfunction | Billable |
| I27.848 | Other Fontan-associated condition | Billable |
| I27.849 | Fontan related circulation, unspecified | Billable |
| I27.89 | Other specified pulmonary heart diseases | Billable |
| I27.9 | Pulmonary heart disease, unspecified | Billable |
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Reviewed by the PayerReady Medical Coding Team
Verified against the CMS 2026 code set on May 31, 2026.
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