Systemic atrophies primarily affecting the central nervous system
33 codes in this section
About Section G10-G14
Section G10-G14 (G10-G14) covers systemic atrophies primarily affecting the central nervous system. It sits within the Diseases of the nervous system chapter (G00-G99). This section contains 33 ICD-10-CM codes, 28 billable diagnoses you can submit on a claim, and 5 non-billable header codes used to organize the hierarchy.
Codes are organized below by 3-character root. Click the root to see all subcodes underneath it, or click any individual code for full coverage data, payer policies, and linked CPT procedures.
Codes in G10-G14
Grouped by 3-character root code. Click any code for full detail.
| G11.0 | Congenital nonprogressive ataxia | Billable |
| G11.1 | Early-onset cerebellar ataxia | Header |
| G11.10 | Early-onset cerebellar ataxia, unspecified | Billable |
| G11.11 | Friedreich ataxia | Billable |
| G11.19 | Other early-onset cerebellar ataxia | Billable |
| G11.2 | Late-onset cerebellar ataxia | Billable |
| G11.3 | Cerebellar ataxia with defective DNA repair | Billable |
| G11.4 | Hereditary spastic paraplegia | Billable |
| G11.5 | Hypomyelination - hypogonadotropic hypogonadism - hypodontia | Billable |
| G11.6 | Leukodystrophy with vanishing white matter disease | Billable |
| G11.8 | Other hereditary ataxias | Billable |
| G11.9 | Hereditary ataxia, unspecified | Billable |
| G12.0 | Infantile spinal muscular atrophy, type I [Werdnig-Hoffman] | Billable |
| G12.1 | Other inherited spinal muscular atrophy | Billable |
| G12.2 | Motor neuron disease | Header |
| G12.20 | Motor neuron disease, unspecified | Billable |
| G12.21 | Amyotrophic lateral sclerosis | Billable |
| G12.22 | Progressive bulbar palsy | Billable |
| G12.23 | Primary lateral sclerosis | Billable |
| G12.24 | Familial motor neuron disease | Billable |
| G12.25 | Progressive spinal muscle atrophy | Billable |
| G12.29 | Other motor neuron disease | Billable |
| G12.8 | Other spinal muscular atrophies and related syndromes | Billable |
| G12.9 | Spinal muscular atrophy, unspecified | Billable |
| G13.0 | Paraneoplastic neuromyopathy and neuropathy | Billable |
| G13.1 | Other systemic atrophy primarily affecting central nervous system in neoplastic disease | Billable |
| G13.2 | Systemic atrophy primarily affecting the central nervous system in myxedema | Billable |
| G13.8 | Systemic atrophy primarily affecting central nervous system in other diseases classified elsewhere | Billable |
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Reviewed by the PayerReady Medical Coding Team
Verified against the CMS 2026 code set on May 31, 2026.
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