ICD-10-CM 2026 · Effective October 1, 2025

ICD-10 G11.3

Billable / Specific HCC v28: 72 CC

Cerebellar ataxia with defective DNA repair

G11
Block
1
Synonyms
549
LCDs
30
Payer Policies
80
Linked CPTs

About ICD-10-CM G11.3

ICD-10-CM code G11.3 represents Cerebellar ataxia with defective DNA repair. This is a billable/specific code in the Nervous System chapter (block G11). The 2026 edition of ICD-10-CM G11.3 became effective on October 1, 2025.

Coding Tips for G11.3

Specialist guidance from the PayerReady Medical Coding Team. Specificity warnings, HCC capture rules, sequencing notes.

HCC capture: document with MEAT each year

G11.3 is a CMS-HCC v28 risk-adjustment code (category 72). To count for the patient Risk Adjustment Factor (RAF), document the diagnosis with MEAT language each calendar year: Monitored, Evaluated, Assessed, Treated. A diagnosis on the problem list alone does not satisfy CMS RADV audit standards. Include the diagnosis in the assessment with current status and current treatment plan.

Inpatient DRG impact: CC

G11.3 is designated CC for MS-DRG grouping. On inpatient claims, this code can shift the DRG to the with-CC variant when documented as a present-on-admission secondary diagnosis. Hospital CDI programs flag CC opportunities during chart review. Failure to capture this code may leave 30 to 80 percent of the inpatient stay revenue unrealized.

Inclusion Terms / Approximate Synonyms

Clinical terms and conditions classified under G11.3. Per CMS ICD-10-CM Tabular 2026.

  • Ataxia telangiectasia [Louis-Bar]

Type 2 Excludes

Not included here, the excluded code is not part of G11.3, but a patient may have both conditions at the same time. Both codes may be coded together when applicable.

  • Cockayne's syndrome (Q87.19)
  • other disorders of purine and pyrimidine metabolism (E79.-)
  • xeroderma pigmentosum (Q82.1)

Medicare Advantage HCC Impact

CMS-HCC v28 (current)
Category 72
ESRD-HCC
Category 72
RxHCC (Part D)
Category 72

Capture this diagnosis annually for accurate risk adjustment. Missed HCC captures are the #1 revenue leak in Medicare Advantage risk programs.

Inpatient DRG Impact, CC

codes Cerebellar ataxia with defective DNA repair. As a Complication/Comorbidity (CC), this contributes to DRG severity adjustment when documented alongside the principal diagnosis.

Medicare LCD Coverage for G11.3

Local Coverage Determinations (LCDs) from CMS MACs that list G11.3 as a covered diagnosis.

549 LCDs

Showing top 10 of 549 total . Click a CPT for full coverage scope.

CMS LCD: Billing and Coding: Nerve Conduction Studies and Electromyography
Article ID: 57668, Effective: 2025-10-01 00:00:00, 1629 covered, 0 non-covered
CPT 95909 →
CMS LCD: Billing and Coding: Nerve Conduction Studies and Electromyography
Article ID: 57668, Effective: 2025-10-01 00:00:00, 1629 covered, 0 non-covered
CPT 95887 →
CMS LCD: Billing and Coding: Nerve Conduction Studies and Electromyography
Article ID: 57668, Effective: 2025-10-01 00:00:00, 1629 covered, 0 non-covered
CPT 95912 →
CMS LCD: Billing and Coding: Nerve Conduction Studies and Electromyography
Article ID: 57668, Effective: 2025-10-01 00:00:00, 1629 covered, 0 non-covered
CPT 95999 →
CMS LCD: Billing and Coding: Nerve Conduction Studies and Electromyography
Article ID: 57668, Effective: 2025-10-01 00:00:00, 1629 covered, 0 non-covered
CPT 95910 →
CMS LCD: Billing and Coding: Nerve Conduction Studies and Electromyography
Article ID: 57668, Effective: 2025-10-01 00:00:00, 1629 covered, 0 non-covered
CPT 95870 →
CMS LCD: Billing and Coding: Nerve Conduction Studies and Electromyography
Article ID: 57668, Effective: 2025-10-01 00:00:00, 1629 covered, 0 non-covered
CPT 95860 →
CMS LCD: Billing and Coding: Nerve Conduction Studies and Electromyography
Article ID: 57668, Effective: 2025-10-01 00:00:00, 1629 covered, 0 non-covered
CPT 95913 →
CMS LCD: Billing and Coding: Nerve Conduction Studies and Electromyography
Article ID: 57668, Effective: 2025-10-01 00:00:00, 1629 covered, 0 non-covered
CPT 95869 →
CMS LCD: Billing and Coding: Nerve Conduction Studies and Electromyography
Article ID: 57668, Effective: 2025-10-01 00:00:00, 1629 covered, 0 non-covered
CPT G0255 →

Commercial Payer Coverage

Coverage policies from major commercial payers referencing G11.3.

30 policies

1 Cigna

Electrodiagnostic Testing (EMG/NCV) - (CPG129)
Policy ID: CPG129_EMG_NCV_SSEP

5 Medicare

External Infusion Pumps - Policy Article
Policy ID: ART-52507
Intravenous Immune Globulin - Policy Article
Policy ID: ART-52509
Billing and Coding: Home Health Occupational Therapy
Policy ID: ART-53057
Billing and Coding: Outpatient Occupational Therapy
Policy ID: ART-53064
Billing and Coding: Outpatient Physical Therapy
Policy ID: ART-53065

CPT Codes Commonly Billed with G11.3

Procedures frequently paired with this diagnosis based on PayerReady's Dx↔Px linkage data.

80 linkages
  • 95926 CMS LCD: Billing and Coding: Somatosensory Testing CMS LCD
  • 95925 CMS LCD: Billing and Coding: Somatosensory Testing CMS LCD
  • 95938 CMS LCD: Billing and Coding: Somatosensory Testing CMS LCD
  • 95927 CMS LCD: Billing and Coding: Somatosensory Testing CMS LCD
  • 29405 CMS LCD: Billing and Coding: Outpatient Physical Therapy CMS LCD
  • 95992 CMS LCD: Billing and Coding: Outpatient Physical Therapy CMS LCD
  • 29280 CMS LCD: Billing and Coding: Outpatient Physical Therapy CMS LCD
  • 97010 CMS LCD: Billing and Coding: Outpatient Physical Therapy CMS LCD
  • 29515 CMS LCD: Billing and Coding: Outpatient Physical Therapy CMS LCD
  • 97550 CMS LCD: Billing and Coding: Outpatient Physical Therapy CMS LCD

Convert G11.3 to ICD-9-CM

Per CMS General Equivalence Mappings (GEMs), useful for legacy data review and historical claim analysis.

ICD-10ICD-9Mapping Flags
G11.3 3348 10000

Flags format (5 digits): Approximate · No Map · Combination · Scenario · Choice List. Source: CMS 2017 GEMs (final version).

ICD-10 G11.3, Billing FAQ

Is ICD-10 code G11.3 billable? +

Yes, G11.3 is a billable ICD-10-CM code that can appear as a primary or secondary diagnosis on claims.

What other names or terms map to G11.3? +

ICD-10 G11.3 includes: Ataxia telangiectasia [Louis-Bar].

What codes are Type 2 Excludes for G11.3? +

Type 2 Excludes (may be coded together when both conditions exist): Cockayne's syndrome (Q87.19); other disorders of purine and pyrimidine metabolism (E79.-); xeroderma pigmentosum (Q82.1)

Does G11.3 affect Medicare Advantage HCC risk adjustment? +

Yes. G11.3 maps to CMS-HCC v28 category 72. Capture this diagnosis annually for accurate Medicare Advantage risk score.

Is G11.3 a CC or MCC for inpatient DRG? +

Yes, this code is designated as CC. Documenting as a secondary diagnosis on inpatient claims can shift the DRG to a higher-weighted category.

What CPT codes are commonly billed with G11.3? +

Procedures frequently paired with G11.3 include: 95926, 95925, 95938, 95927, 29405.

What ICD-9 codes does G11.3 map to? +

Per CMS GEMs, G11.3 maps to ICD-9 codes: 3348. Useful for legacy data review and historical claim analysis.

Get the full PayerReady toolkit

Free access to CPT/ICD-10 lookup, denial appeals, fee comparator, and claim auditing with credentialing enrollment.

Start free →

Run this code through our claim audit tool

Check NCCI bundling, MUE limits, and modifier logic before submission.

Try the auditor →

Did this page help?

Quick signal so we know what to improve.

Thanks!

If you want a code reference page that doesn't exist yet, email coding@payerready.com.

Sorry to hear that.

Tell us what's missing or wrong: coding@payerready.com. We respond within 5 business days.

Reviewed by the PayerReady Medical Coding Team

Verified against the CMS 2026 code set on May 31, 2026.

Powered by 11K CPT · 98K ICD-10 · 860K MPFS rates · 4.5M NCCI edits · 9.5M NPIs. Our data methodology · About our coding team

Faster Approvals

Ready to Cut Your Enrollment Timeline in Half?

Join providers in all 50 states who handed off credentialing to a dedicated specialist. Create your free account in minutes and start enrolling the same day.

All 50 States Covered
No Long-Term Contracts
HIPAA HIPAA Compliant Platform
Dedicated Specialist Included