ICD-10-CM Section · Q90-Q99

Chromosomal abnormalities, not elsewhere classified

88 codes in this section

88
Total Codes
74
Billable
14
Header (Non-Billable)
9
Top-Level Codes

About Section Q90-Q99

Section Q90-Q99 (Q90-Q99) covers chromosomal abnormalities, not elsewhere classified. It sits within the Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders chapter (Q00-QA0). This section contains 88 ICD-10-CM codes, 74 billable diagnoses you can submit on a claim, and 14 non-billable header codes used to organize the hierarchy.

Codes are organized below by 3-character root. Click the root to see all subcodes underneath it, or click any individual code for full coverage data, payer policies, and linked CPT procedures.

Codes in Q90-Q99

Grouped by 3-character root code. Click any code for full detail.

Q90 Down syndrome
4 subcodes
Q90.0 Trisomy 21, nonmosaicism (meiotic nondisjunction) Billable
Q90.1 Trisomy 21, mosaicism (mitotic nondisjunction) Billable
Q90.2 Trisomy 21, translocation Billable
Q90.9 Down syndrome, unspecified Billable
Q91 Trisomy 18 and Trisomy 13
8 subcodes
Q91.0 Trisomy 18, nonmosaicism (meiotic nondisjunction) Billable
Q91.1 Trisomy 18, mosaicism (mitotic nondisjunction) Billable
Q91.2 Trisomy 18, translocation Billable
Q91.3 Trisomy 18, unspecified Billable
Q91.4 Trisomy 13, nonmosaicism (meiotic nondisjunction) Billable
Q91.5 Trisomy 13, mosaicism (mitotic nondisjunction) Billable
Q91.6 Trisomy 13, translocation Billable
Q91.7 Trisomy 13, unspecified Billable
Q92 Other trisomies and partial trisomies of the autosomes, not elsewhere classified
10 subcodes
Q92.0 Whole chromosome trisomy, nonmosaicism (meiotic nondisjunction) Billable
Q92.1 Whole chromosome trisomy, mosaicism (mitotic nondisjunction) Billable
Q92.2 Partial trisomy Billable
Q92.5 Duplications with other complex rearrangements Billable
Q92.6 Marker chromosomes Header
Q92.61 Marker chromosomes in normal individual Billable
Q92.62 Marker chromosomes in abnormal individual Billable
Q92.7 Triploidy and polyploidy Billable
Q92.8 Other specified trisomies and partial trisomies of autosomes Billable
Q92.9 Trisomy and partial trisomy of autosomes, unspecified Billable
Q93 Monosomies and deletions from the autosomes, not elsewhere classified
16 subcodes
Q93.0 Whole chromosome monosomy, nonmosaicism (meiotic nondisjunction) Billable
Q93.1 Whole chromosome monosomy, mosaicism (mitotic nondisjunction) Billable
Q93.2 Chromosome replaced with ring, dicentric or isochromosome Billable
Q93.3 Deletion of short arm of chromosome 4 Billable
Q93.4 Deletion of short arm of chromosome 5 Billable
Q93.5 Other deletions of part of a chromosome Header
Q93.51 Angelman syndrome Billable
Q93.52 Phelan-McDermid syndrome Billable
Q93.59 Other deletions of part of a chromosome Billable
Q93.7 Deletions with other complex rearrangements Billable
Q93.8 Other deletions from the autosomes Header
Q93.81 Velo-cardio-facial syndrome Billable
Q93.82 Williams syndrome Billable
Q93.88 Other microdeletions Billable
Q93.89 Other deletions from the autosomes Billable
Q93.9 Deletion from autosomes, unspecified Billable
Q95 Balanced rearrangements and structural markers, not elsewhere classified
7 subcodes
Q95.0 Balanced translocation and insertion in normal individual Billable
Q95.1 Chromosome inversion in normal individual Billable
Q95.2 Balanced autosomal rearrangement in abnormal individual Billable
Q95.3 Balanced sex/autosomal rearrangement in abnormal individual Billable
Q95.5 Individual with autosomal fragile site Billable
Q95.8 Other balanced rearrangements and structural markers Billable
Q95.9 Balanced rearrangement and structural marker, unspecified Billable
Q96 Turner's syndrome
7 subcodes
Q96.0 Karyotype 45, X Billable
Q96.1 Karyotype 46, X iso (Xq) Billable
Q96.2 Karyotype 46, X with abnormal sex chromosome, except iso (Xq) Billable
Q96.3 Mosaicism, 45, X/46, XX or XY Billable
Q96.4 Mosaicism, 45, X/other cell line(s) with abnormal sex chromosome Billable
Q96.8 Other variants of Turner's syndrome Billable
Q96.9 Turner's syndrome, unspecified Billable
Q97 Other sex chromosome abnormalities, female phenotype, not elsewhere classified
6 subcodes
Q97.0 Karyotype 47, XXX Billable
Q97.1 Female with more than three X chromosomes Billable
Q97.2 Mosaicism, lines with various numbers of X chromosomes Billable
Q97.3 Female with 46, XY karyotype Billable
Q97.8 Other specified sex chromosome abnormalities, female phenotype Billable
Q97.9 Sex chromosome abnormality, female phenotype, unspecified Billable
Q98 Other sex chromosome abnormalities, male phenotype, not elsewhere classified
9 subcodes
Q98.0 Klinefelter syndrome karyotype 47, XXY Billable
Q98.1 Klinefelter syndrome, male with more than two X chromosomes Billable
Q98.3 Other male with 46, XX karyotype Billable
Q98.4 Klinefelter syndrome, unspecified Billable
Q98.5 Karyotype 47, XYY Billable
Q98.6 Male with structurally abnormal sex chromosome Billable
Q98.7 Male with sex chromosome mosaicism Billable
Q98.8 Other specified sex chromosome abnormalities, male phenotype Billable
Q98.9 Sex chromosome abnormality, male phenotype, unspecified Billable
Q99 Other chromosome abnormalities, not elsewhere classified
12 subcodes
Q99.0 Chimera 46, XX/46, XY Billable
Q99.1 46, XX true hermaphrodite Billable
Q99.2 Fragile X chromosome Billable
Q99.8 Other specified chromosome abnormalities Header
Q99.81 Usher syndrome Header
Q99.811 Usher syndrome, type 1 Billable
Q99.812 Usher syndrome, type 2 Billable
Q99.813 Usher syndrome, type 3 Billable
Q99.818 Other Usher syndrome Billable
Q99.819 Usher syndrome, unspecified Billable
Q99.89 Other specified chromosome abnormalities Billable
Q99.9 Chromosomal abnormality, unspecified Billable

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Verified against the CMS 2026 code set on May 31, 2026.

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