ICD-10 Q99.1
Billable / Specific46, XX true hermaphrodite
About ICD-10-CM Q99.1
ICD-10-CM code Q99.1 represents 46, XX true hermaphrodite. This is a billable/specific code in the Congenital Malformations chapter (block Q99). The 2026 edition of ICD-10-CM Q99.1 became effective on October 1, 2025.
Inclusion Terms / Approximate Synonyms
Clinical terms and conditions classified under Q99.1. Per CMS ICD-10-CM Tabular 2026.
- 46, XX with streak gonads
- 46, XY with streak gonads
- Pure gonadal dysgenesis
Medicare LCD Coverage for Q99.1
Local Coverage Determinations (LCDs) from CMS MACs that list Q99.1 as a covered diagnosis.
This doesn't mean the code isn't covered, it means no MAC has issued a Local Coverage Determination naming this specific code. Coverage may still apply under National Coverage Determinations or general medical-necessity rules.
Commercial Payer Coverage
Coverage policies from major commercial payers referencing Q99.1.
Our payer policy database covers Aetna, Cigna, Anthem, BCBS, Humana, and Medicare Advantage plans, but Q99.1 doesn't currently appear in any indexed policy. The code may still be covered under standard plan benefits.
CPT Codes Commonly Billed with Q99.1
Procedures frequently paired with this diagnosis based on PayerReady's Dx↔Px linkage data.
We don't have CPT pairings indexed for this specific code yet. Use the CPT search above to find common procedures, or check your payer's published medical policy for code-specific guidance.
Convert Q99.1 to ICD-9-CM
Per CMS General Equivalence Mappings (GEMs), useful for legacy data review and historical claim analysis.
| ICD-10 | ICD-9 | Mapping Flags |
|---|---|---|
| Q99.1 | 75881 | 10000 |
Flags format (5 digits): Approximate · No Map · Combination · Scenario · Choice List. Source: CMS 2017 GEMs (final version).
Codes Adjacent To Q99.1
Other codes in section Q90-Q99 (Chromosomal abnormalities, not elsewhere classified).
ICD-10 Q99.1, Billing FAQ
Is ICD-10 code Q99.1 billable? +
Yes, Q99.1 is a billable ICD-10-CM code that can appear as a primary or secondary diagnosis on claims.
What other names or terms map to Q99.1? +
ICD-10 Q99.1 includes: 46, XX with streak gonads; 46, XY with streak gonads; Pure gonadal dysgenesis.
What ICD-9 codes does Q99.1 map to? +
Per CMS GEMs, Q99.1 maps to ICD-9 codes: 75881. Useful for legacy data review and historical claim analysis.
Get the full PayerReady toolkit
Free access to CPT/ICD-10 lookup, denial appeals, fee comparator, and claim auditing with credentialing enrollment.
Start free →Run this code through our claim audit tool
Check NCCI bundling, MUE limits, and modifier logic before submission.
Try the auditor →Did this page help?
Quick signal so we know what to improve.
If you want a code reference page that doesn't exist yet, email coding@payerready.com.
Tell us what's missing or wrong: coding@payerready.com. We respond within 5 business days.
Reviewed by the PayerReady Medical Coding Team
Verified against the CMS 2026 code set on July 16, 2026.
Powered by 11K CPT · 98K ICD-10 · 860K MPFS rates · 4.5M NCCI edits · 9.5M NPIs. Our data methodology · About our coding team