ICD-10-CM Section · M30-M36
Systemic connective tissue disorders
101 codes in this section
101
Total Codes
84
Billable
17
Header (Non-Billable)
7
Top-Level Codes
About Section M30-M36
Section M30-M36 (M30-M36) covers systemic connective tissue disorders. It sits within the Diseases of the musculoskeletal system and connective tissue chapter (M00-M99). This section contains 101 ICD-10-CM codes, 84 billable diagnoses you can submit on a claim, and 17 non-billable header codes used to organize the hierarchy.
Codes are organized below by 3-character root. Click the root to see all subcodes underneath it, or click any individual code for full coverage data, payer policies, and linked CPT procedures.
Codes in M30-M36
Grouped by 3-character root code. Click any code for full detail.
M30
Polyarteritis nodosa and related conditions
5 subcodes
| M30.0 | Polyarteritis nodosa | Billable |
| M30.1 | Polyarteritis with lung involvement [Churg-Strauss] | Billable |
| M30.2 | Juvenile polyarteritis | Billable |
| M30.3 | Mucocutaneous lymph node syndrome [Kawasaki] | Billable |
| M30.8 | Other conditions related to polyarteritis nodosa | Billable |
M31
Other necrotizing vasculopathies
15 subcodes
| M31.0 | Hypersensitivity angiitis | Billable |
| M31.1 | Thrombotic microangiopathy | Header |
| M31.10 | Thrombotic microangiopathy, unspecified | Billable |
| M31.11 | Hematopoietic stem cell transplantation-associated thrombotic microangiopathy [HSCT-TMA] | Billable |
| M31.19 | Other thrombotic microangiopathy | Billable |
| M31.2 | Lethal midline granuloma | Billable |
| M31.3 | Wegener's granulomatosis | Header |
| M31.30 | Wegener's granulomatosis without renal involvement | Billable |
| M31.31 | Wegener's granulomatosis with renal involvement | Billable |
| M31.4 | Aortic arch syndrome [Takayasu] | Billable |
| M31.5 | Giant cell arteritis with polymyalgia rheumatica | Billable |
| M31.6 | Other giant cell arteritis | Billable |
| M31.7 | Microscopic polyangiitis | Billable |
| M31.8 | Other specified necrotizing vasculopathies | Billable |
| M31.9 | Necrotizing vasculopathy, unspecified | Billable |
M32
Systemic lupus erythematosus (SLE)
11 subcodes
| M32.0 | Drug-induced systemic lupus erythematosus | Billable |
| M32.1 | Systemic lupus erythematosus with organ or system involvement | Header |
| M32.10 | Systemic lupus erythematosus, organ or system involvement unspecified | Billable |
| M32.11 | Endocarditis in systemic lupus erythematosus | Billable |
| M32.12 | Pericarditis in systemic lupus erythematosus | Billable |
| M32.13 | Lung involvement in systemic lupus erythematosus | Billable |
| M32.14 | Glomerular disease in systemic lupus erythematosus | Billable |
| M32.15 | Tubulo-interstitial nephropathy in systemic lupus erythematosus | Billable |
| M32.19 | Other organ or system involvement in systemic lupus erythematosus | Billable |
| M32.8 | Other forms of systemic lupus erythematosus | Billable |
| M32.9 | Systemic lupus erythematosus, unspecified | Billable |
M33
Dermatopolymyositis
23 subcodes
| M33.0 | Juvenile dermatomyositis | Header |
| M33.00 | Juvenile dermatomyositis, organ involvement unspecified | Billable |
| M33.01 | Juvenile dermatomyositis with respiratory involvement | Billable |
| M33.02 | Juvenile dermatomyositis with myopathy | Billable |
| M33.03 | Juvenile dermatomyositis without myopathy | Billable |
| M33.09 | Juvenile dermatomyositis with other organ involvement | Billable |
| M33.1 | Other dermatomyositis | Header |
| M33.10 | Other dermatomyositis, organ involvement unspecified | Billable |
| M33.11 | Other dermatomyositis with respiratory involvement | Billable |
| M33.12 | Other dermatomyositis with myopathy | Billable |
| M33.13 | Other dermatomyositis without myopathy | Billable |
| M33.19 | Other dermatomyositis with other organ involvement | Billable |
| M33.2 | Polymyositis | Header |
| M33.20 | Polymyositis, organ involvement unspecified | Billable |
| M33.21 | Polymyositis with respiratory involvement | Billable |
| M33.22 | Polymyositis with myopathy | Billable |
| M33.29 | Polymyositis with other organ involvement | Billable |
| M33.9 | Dermatopolymyositis, unspecified | Header |
| M33.90 | Dermatopolymyositis, unspecified, organ involvement unspecified | Billable |
| M33.91 | Dermatopolymyositis, unspecified with respiratory involvement | Billable |
| M33.92 | Dermatopolymyositis, unspecified with myopathy | Billable |
| M33.93 | Dermatopolymyositis, unspecified without myopathy | Billable |
| M33.99 | Dermatopolymyositis, unspecified with other organ involvement | Billable |
M34
Systemic sclerosis [scleroderma]
9 subcodes
| M34.0 | Progressive systemic sclerosis | Billable |
| M34.1 | CR(E)ST syndrome | Billable |
| M34.2 | Systemic sclerosis induced by drug and chemical | Billable |
| M34.8 | Other forms of systemic sclerosis | Header |
| M34.81 | Systemic sclerosis with lung involvement | Billable |
| M34.82 | Systemic sclerosis with myopathy | Billable |
| M34.83 | Systemic sclerosis with polyneuropathy | Billable |
| M34.89 | Other systemic sclerosis | Billable |
| M34.9 | Systemic sclerosis, unspecified | Billable |
M35
Other systemic involvement of connective tissue
25 subcodes
| M35.0 | Sjogren syndrome | Header |
| M35.00 | Sjogren syndrome, unspecified | Billable |
| M35.01 | Sjogren syndrome with keratoconjunctivitis | Billable |
| M35.02 | Sjogren syndrome with lung involvement | Billable |
| M35.03 | Sjogren syndrome with myopathy | Billable |
| M35.04 | Sjogren syndrome with tubulo-interstitial nephropathy | Billable |
| M35.05 | Sjogren syndrome with inflammatory arthritis | Billable |
| M35.06 | Sjogren syndrome with peripheral nervous system involvement | Billable |
| M35.07 | Sjogren syndrome with central nervous system involvement | Billable |
| M35.08 | Sjogren syndrome with gastrointestinal involvement | Billable |
| M35.09 | Sjogren syndrome with other organ involvement | Billable |
| M35.0A | Sjogren syndrome with glomerular disease | Billable |
| M35.0B | Sjogren syndrome with vasculitis | Billable |
| M35.0C | Sjogren syndrome with dental involvement | Billable |
| M35.1 | Other overlap syndromes | Billable |
| M35.2 | Behcet's disease | Billable |
| M35.3 | Polymyalgia rheumatica | Billable |
| M35.4 | Diffuse (eosinophilic) fasciitis | Billable |
| M35.5 | Multifocal fibrosclerosis | Billable |
| M35.6 | Relapsing panniculitis [Weber-Christian] | Billable |
| M35.7 | Hypermobility syndrome | Billable |
| M35.8 | Other specified systemic involvement of connective tissue | Header |
| M35.81 | Multisystem inflammatory syndrome | Billable |
| M35.89 | Other specified systemic involvement of connective tissue | Billable |
| M35.9 | Systemic involvement of connective tissue, unspecified | Billable |
M36
Systemic disorders of connective tissue in diseases classified elsewhere
6 subcodes
| M36.0 | Dermato(poly)myositis in neoplastic disease | Billable |
| M36.1 | Arthropathy in neoplastic disease | Billable |
| M36.2 | Hemophilic arthropathy | Billable |
| M36.3 | Arthropathy in other blood disorders | Billable |
| M36.4 | Arthropathy in hypersensitivity reactions classified elsewhere | Billable |
| M36.8 | Systemic disorders of connective tissue in other diseases classified elsewhere | Billable |
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Verified against the CMS 2026 code set on May 31, 2026.
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