ICD-10 N01
Non-Billable HeaderRapidly progressive nephritic syndrome
About ICD-10-CM N01
ICD-10-CM code N01 represents Rapidly progressive nephritic syndrome. This is a non-billable header code in the Genitourinary System chapter (block N01). The 2026 edition of ICD-10-CM N01 became effective on October 1, 2025. Non-billable codes cannot be used as a primary or secondary diagnosis on a claim, use a more specific child code instead.
Type 1 Excludes
Pure excludes, these codes can never be coded together with N01. The conditions are mutually exclusive (e.g., congenital vs acquired forms).
- nephritic syndrome NOS (N05.-)
Includes
- rapidly progressive glomerular disease
- rapidly progressive glomerulonephritis
- rapidly progressive nephritis
Medicare LCD Coverage for N01
Local Coverage Determinations (LCDs) from CMS MACs that list N01 as a covered diagnosis.
This doesn't mean the code isn't covered, it means no MAC has issued a Local Coverage Determination naming this specific code. Coverage may still apply under National Coverage Determinations or general medical-necessity rules.
Commercial Payer Coverage
Coverage policies from major commercial payers referencing N01.
Our payer policy database covers Aetna, Cigna, Anthem, BCBS, Humana, and Medicare Advantage plans, but N01 doesn't currently appear in any indexed policy. The code may still be covered under standard plan benefits.
CPT Codes Commonly Billed with N01
Procedures frequently paired with this diagnosis based on PayerReady's Dx↔Px linkage data.
We don't have CPT pairings indexed for this specific code yet. Use the CPT search above to find common procedures, or check your payer's published medical policy for code-specific guidance.
Codes Adjacent To N01
Other codes in section N00-N08 (Glomerular diseases).
ICD-10 N01, Billing FAQ
Is ICD-10 code N01 billable? +
No, N01 is a non-billable header code. Use a more specific child code from block N01 when submitting claims.
What codes are Type 1 Excludes for N01? +
Type 1 Excludes (never code together with N01): nephritic syndrome NOS (N05.-)
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Reviewed by the PayerReady Medical Coding Team
Verified against the CMS 2026 code set on June 1, 2026.
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