ICD-10 E00
Non-Billable HeaderCongenital iodine-deficiency syndrome
About ICD-10-CM E00
ICD-10-CM code E00 represents Congenital iodine-deficiency syndrome. This is a non-billable header code in the Endocrine, Nutritional, and Metabolic chapter (block E00). The 2026 edition of ICD-10-CM E00 became effective on October 1, 2025. Non-billable codes cannot be used as a primary or secondary diagnosis on a claim, use a more specific child code instead.
Type 1 Excludes
Pure excludes, these codes can never be coded together with E00. The conditions are mutually exclusive (e.g., congenital vs acquired forms).
- subclinical iodine-deficiency hypothyroidism (E02)
Use Additional Code
When coding E00, also report these additional codes when applicable.
- code (F70-F79) to identify associated intellectual disabilities.
Medicare LCD Coverage for E00
Local Coverage Determinations (LCDs) from CMS MACs that list E00 as a covered diagnosis.
This doesn't mean the code isn't covered, it means no MAC has issued a Local Coverage Determination naming this specific code. Coverage may still apply under National Coverage Determinations or general medical-necessity rules.
Commercial Payer Coverage
Coverage policies from major commercial payers referencing E00.
Our payer policy database covers Aetna, Cigna, Anthem, BCBS, Humana, and Medicare Advantage plans, but E00 doesn't currently appear in any indexed policy. The code may still be covered under standard plan benefits.
CPT Codes Commonly Billed with E00
Procedures frequently paired with this diagnosis based on PayerReady's Dx↔Px linkage data.
We don't have CPT pairings indexed for this specific code yet. Use the CPT search above to find common procedures, or check your payer's published medical policy for code-specific guidance.
Codes Adjacent To E00
Other codes in section E00-E07 (Disorders of thyroid gland).
ICD-10 E00, Billing FAQ
Is ICD-10 code E00 billable? +
No, E00 is a non-billable header code. Use a more specific child code from block E00 when submitting claims.
What codes are Type 1 Excludes for E00? +
Type 1 Excludes (never code together with E00): subclinical iodine-deficiency hypothyroidism (E02)
Get the full PayerReady toolkit
Free access to CPT/ICD-10 lookup, denial appeals, fee comparator, and claim auditing with credentialing enrollment.
Start free →Run this code through our claim audit tool
Check NCCI bundling, MUE limits, and modifier logic before submission.
Try the auditor →Did this page help?
Quick signal so we know what to improve.
If you want a code reference page that doesn't exist yet, email coding@payerready.com.
Tell us what's missing or wrong: coding@payerready.com. We respond within 5 business days.
Reviewed by the PayerReady Medical Coding Team
Verified against the CMS 2026 code set on May 31, 2026.
Powered by 11K CPT · 98K ICD-10 · 860K MPFS rates · 4.5M NCCI edits · 9.5M NPIs. Our data methodology · About our coding team