Congenital malformations of genital organs
115 codes in this section
About Section Q50-Q56
Section Q50-Q56 (Q50-Q56) covers congenital malformations of genital organs. It sits within the Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders chapter (Q00-QA0). This section contains 115 ICD-10-CM codes, 91 billable diagnoses you can submit on a claim, and 24 non-billable header codes used to organize the hierarchy.
Codes are organized below by 3-character root. Click the root to see all subcodes underneath it, or click any individual code for full coverage data, payer policies, and linked CPT procedures.
Codes in Q50-Q56
Grouped by 3-character root code. Click any code for full detail.
| Q50.0 | Congenital absence of ovary | Header |
| Q50.01 | Congenital absence of ovary, unilateral | Billable |
| Q50.02 | Congenital absence of ovary, bilateral | Billable |
| Q50.1 | Developmental ovarian cyst | Billable |
| Q50.2 | Congenital torsion of ovary | Billable |
| Q50.3 | Other congenital malformations of ovary | Header |
| Q50.31 | Accessory ovary | Billable |
| Q50.32 | Ovarian streak | Billable |
| Q50.39 | Other congenital malformation of ovary | Billable |
| Q50.4 | Embryonic cyst of fallopian tube | Billable |
| Q50.5 | Embryonic cyst of broad ligament | Billable |
| Q50.6 | Other congenital malformations of fallopian tube and broad ligament | Billable |
| Q51.0 | Agenesis and aplasia of uterus | Billable |
| Q51.1 | Doubling of uterus with doubling of cervix and vagina | Header |
| Q51.10 | Doubling of uterus with doubling of cervix and vagina without obstruction | Billable |
| Q51.11 | Doubling of uterus with doubling of cervix and vagina with obstruction | Billable |
| Q51.2 | Other doubling of uterus | Header |
| Q51.21 | Complete doubling of uterus | Billable |
| Q51.22 | Partial doubling of uterus | Billable |
| Q51.28 | Other and unspecified doubling of uterus | Billable |
| Q51.3 | Bicornate uterus | Billable |
| Q51.4 | Unicornate uterus | Billable |
| Q51.5 | Agenesis and aplasia of cervix | Billable |
| Q51.6 | Embryonic cyst of cervix | Billable |
| Q51.7 | Congenital fistulae between uterus and digestive and urinary tracts | Billable |
| Q51.8 | Other congenital malformations of uterus and cervix | Header |
| Q51.81 | Other congenital malformations of uterus | Header |
| Q51.810 | Arcuate uterus | Billable |
| Q51.811 | Hypoplasia of uterus | Billable |
| Q51.818 | Other congenital malformations of uterus | Billable |
| Q51.82 | Other congenital malformations of cervix | Header |
| Q51.820 | Cervical duplication | Billable |
| Q51.821 | Hypoplasia of cervix | Billable |
| Q51.828 | Other congenital malformations of cervix | Billable |
| Q51.9 | Congenital malformation of uterus and cervix, unspecified | Billable |
| Q52.0 | Congenital absence of vagina | Billable |
| Q52.1 | Doubling of vagina | Header |
| Q52.10 | Doubling of vagina, unspecified | Billable |
| Q52.11 | Transverse vaginal septum | Billable |
| Q52.12 | Longitudinal vaginal septum | Header |
| Q52.120 | Longitudinal vaginal septum, nonobstructing | Billable |
| Q52.121 | Longitudinal vaginal septum, obstructing, right side | Billable |
| Q52.122 | Longitudinal vaginal septum, obstructing, left side | Billable |
| Q52.123 | Longitudinal vaginal septum, microperforate, right side | Billable |
| Q52.124 | Longitudinal vaginal septum, microperforate, left side | Billable |
| Q52.129 | Other and unspecified longitudinal vaginal septum | Billable |
| Q52.2 | Congenital rectovaginal fistula | Billable |
| Q52.3 | Imperforate hymen | Billable |
| Q52.4 | Other congenital malformations of vagina | Billable |
| Q52.5 | Fusion of labia | Billable |
| Q52.6 | Congenital malformation of clitoris | Billable |
| Q52.7 | Other and unspecified congenital malformations of vulva | Header |
| Q52.70 | Unspecified congenital malformations of vulva | Billable |
| Q52.71 | Congenital absence of vulva | Billable |
| Q52.79 | Other congenital malformations of vulva | Billable |
| Q52.8 | Other specified congenital malformations of female genitalia | Billable |
| Q52.9 | Congenital malformation of female genitalia, unspecified | Billable |
| Q53.0 | Ectopic testis | Header |
| Q53.00 | Ectopic testis, unspecified | Billable |
| Q53.01 | Ectopic testis, unilateral | Billable |
| Q53.02 | Ectopic testes, bilateral | Billable |
| Q53.1 | Undescended testicle, unilateral | Header |
| Q53.10 | Unspecified undescended testicle, unilateral | Billable |
| Q53.11 | Abdominal testis, unilateral | Header |
| Q53.111 | Unilateral intraabdominal testis | Billable |
| Q53.112 | Unilateral inguinal testis | Billable |
| Q53.12 | Ectopic perineal testis, unilateral | Billable |
| Q53.13 | Unilateral high scrotal testis | Billable |
| Q53.2 | Undescended testicle, bilateral | Header |
| Q53.20 | Undescended testicle, unspecified, bilateral | Billable |
| Q53.21 | Abdominal testis, bilateral | Header |
| Q53.211 | Bilateral intraabdominal testes | Billable |
| Q53.212 | Bilateral inguinal testes | Billable |
| Q53.22 | Ectopic perineal testis, bilateral | Billable |
| Q53.23 | Bilateral high scrotal testes | Billable |
| Q53.9 | Undescended testicle, unspecified | Billable |
| Q54.0 | Hypospadias, balanic | Billable |
| Q54.1 | Hypospadias, penile | Billable |
| Q54.2 | Hypospadias, penoscrotal | Billable |
| Q54.3 | Hypospadias, perineal | Billable |
| Q54.4 | Congenital chordee | Billable |
| Q54.8 | Other hypospadias | Billable |
| Q54.9 | Hypospadias, unspecified | Billable |
| Q55.0 | Absence and aplasia of testis | Billable |
| Q55.1 | Hypoplasia of testis and scrotum | Billable |
| Q55.2 | Other and unspecified congenital malformations of testis and scrotum | Header |
| Q55.20 | Unspecified congenital malformations of testis and scrotum | Billable |
| Q55.21 | Polyorchism | Billable |
| Q55.22 | Retractile testis | Billable |
| Q55.23 | Scrotal transposition | Billable |
| Q55.29 | Other congenital malformations of testis and scrotum | Billable |
| Q55.3 | Atresia of vas deferens | Billable |
| Q55.4 | Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate | Billable |
| Q55.5 | Congenital absence and aplasia of penis | Billable |
| Q55.6 | Other congenital malformations of penis | Header |
| Q55.61 | Curvature of penis (lateral) | Billable |
| Q55.62 | Hypoplasia of penis | Billable |
| Q55.63 | Congenital torsion of penis | Billable |
| Q55.64 | Hidden penis | Billable |
| Q55.69 | Other congenital malformation of penis | Billable |
| Q55.7 | Congenital vasocutaneous fistula | Billable |
| Q55.8 | Other specified congenital malformations of male genital organs | Billable |
| Q55.9 | Congenital malformation of male genital organ, unspecified | Billable |
| Q56.0 | Hermaphroditism, not elsewhere classified | Billable |
| Q56.1 | Male pseudohermaphroditism, not elsewhere classified | Billable |
| Q56.2 | Female pseudohermaphroditism, not elsewhere classified | Billable |
| Q56.3 | Pseudohermaphroditism, unspecified | Billable |
| Q56.4 | Indeterminate sex, unspecified | Billable |
Did this page help?
Quick signal so we know what to improve.
If you want a code reference page that doesn't exist yet, email coding@payerready.com.
Tell us what's missing or wrong: coding@payerready.com. We respond within 5 business days.
Reviewed by the PayerReady Medical Coding Team
Verified against the CMS 2026 code set on May 31, 2026.
Powered by 11K CPT · 98K ICD-10 · 860K MPFS rates · 4.5M NCCI edits · 9.5M NPIs. Our data methodology · About our coding team