ICD-10-CM Section · Q20-Q28
Congenital malformations of the circulatory system
118 codes in this section
118
Total Codes
102
Billable
16
Header (Non-Billable)
9
Top-Level Codes
About Section Q20-Q28
Section Q20-Q28 (Q20-Q28) covers congenital malformations of the circulatory system. It sits within the Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders chapter (Q00-QA0). This section contains 118 ICD-10-CM codes, 102 billable diagnoses you can submit on a claim, and 16 non-billable header codes used to organize the hierarchy.
Codes are organized below by 3-character root. Click the root to see all subcodes underneath it, or click any individual code for full coverage data, payer policies, and linked CPT procedures.
Codes in Q20-Q28
Grouped by 3-character root code. Click any code for full detail.
Q20
Congenital malformations of cardiac chambers and connections
9 subcodes
| Q20.0 | Common arterial trunk | Billable |
| Q20.1 | Double outlet right ventricle | Billable |
| Q20.2 | Double outlet left ventricle | Billable |
| Q20.3 | Discordant ventriculoarterial connection | Billable |
| Q20.4 | Double inlet ventricle | Billable |
| Q20.5 | Discordant atrioventricular connection | Billable |
| Q20.6 | Isomerism of atrial appendages | Billable |
| Q20.8 | Other congenital malformations of cardiac chambers and connections | Billable |
| Q20.9 | Congenital malformation of cardiac chambers and connections, unspecified | Billable |
Q21
Congenital malformations of cardiac septa
19 subcodes
| Q21.0 | Ventricular septal defect | Billable |
| Q21.1 | Atrial septal defect | Header |
| Q21.10 | Atrial septal defect, unspecified | Billable |
| Q21.11 | Secundum atrial septal defect | Billable |
| Q21.12 | Patent foramen ovale | Billable |
| Q21.13 | Coronary sinus atrial septal defect | Billable |
| Q21.14 | Superior sinus venosus atrial septal defect | Billable |
| Q21.15 | Inferior sinus venosus atrial septal defect | Billable |
| Q21.16 | Sinus venosus atrial septal defect, unspecified | Billable |
| Q21.19 | Other specified atrial septal defect | Billable |
| Q21.2 | Atrioventricular septal defect | Header |
| Q21.20 | Atrioventricular septal defect, unspecified as to partial or complete | Billable |
| Q21.21 | Partial atrioventricular septal defect | Billable |
| Q21.22 | Transitional atrioventricular septal defect | Billable |
| Q21.23 | Complete atrioventricular septal defect | Billable |
| Q21.3 | Tetralogy of Fallot | Billable |
| Q21.4 | Aortopulmonary septal defect | Billable |
| Q21.8 | Other congenital malformations of cardiac septa | Billable |
| Q21.9 | Congenital malformation of cardiac septum, unspecified | Billable |
Q22
Congenital malformations of pulmonary and tricuspid valves
9 subcodes
| Q22.0 | Pulmonary valve atresia | Billable |
| Q22.1 | Congenital pulmonary valve stenosis | Billable |
| Q22.2 | Congenital pulmonary valve insufficiency | Billable |
| Q22.3 | Other congenital malformations of pulmonary valve | Billable |
| Q22.4 | Congenital tricuspid stenosis | Billable |
| Q22.5 | Ebstein's anomaly | Billable |
| Q22.6 | Hypoplastic right heart syndrome | Billable |
| Q22.8 | Other congenital malformations of tricuspid valve | Billable |
| Q22.9 | Congenital malformation of tricuspid valve, unspecified | Billable |
Q23
Congenital malformations of aortic and mitral valves
10 subcodes
| Q23.0 | Congenital stenosis of aortic valve | Billable |
| Q23.1 | Congenital insufficiency of aortic valve | Billable |
| Q23.2 | Congenital mitral stenosis | Billable |
| Q23.3 | Congenital mitral insufficiency | Billable |
| Q23.4 | Hypoplastic left heart syndrome | Billable |
| Q23.8 | Other congenital malformations of aortic and mitral valves | Header |
| Q23.81 | Bicuspid aortic valve | Billable |
| Q23.82 | Congenital mitral valve cleft leaflet | Billable |
| Q23.88 | Other congenital malformations of aortic and mitral valves | Billable |
| Q23.9 | Congenital malformation of aortic and mitral valves, unspecified | Billable |
Q24
Other congenital malformations of heart
9 subcodes
| Q24.0 | Dextrocardia | Billable |
| Q24.1 | Levocardia | Billable |
| Q24.2 | Cor triatriatum | Billable |
| Q24.3 | Pulmonary infundibular stenosis | Billable |
| Q24.4 | Congenital subaortic stenosis | Billable |
| Q24.5 | Malformation of coronary vessels | Billable |
| Q24.6 | Congenital heart block | Billable |
| Q24.8 | Other specified congenital malformations of heart | Billable |
| Q24.9 | Congenital malformation of heart, unspecified | Billable |
Q25
Congenital malformations of great arteries
25 subcodes
| Q25.0 | Patent ductus arteriosus | Billable |
| Q25.1 | Coarctation of aorta | Billable |
| Q25.2 | Atresia of aorta | Header |
| Q25.21 | Interruption of aortic arch | Billable |
| Q25.29 | Other atresia of aorta | Billable |
| Q25.3 | Supravalvular aortic stenosis | Billable |
| Q25.4 | Other congenital malformations of aorta | Header |
| Q25.40 | Congenital malformation of aorta unspecified | Billable |
| Q25.41 | Absence and aplasia of aorta | Billable |
| Q25.42 | Hypoplasia of aorta | Billable |
| Q25.43 | Congenital aneurysm of aorta | Billable |
| Q25.44 | Congenital dilation of aorta | Billable |
| Q25.45 | Double aortic arch | Billable |
| Q25.46 | Tortuous aortic arch | Billable |
| Q25.47 | Right aortic arch | Billable |
| Q25.48 | Anomalous origin of subclavian artery | Billable |
| Q25.49 | Other congenital malformations of aorta | Billable |
| Q25.5 | Atresia of pulmonary artery | Billable |
| Q25.6 | Stenosis of pulmonary artery | Billable |
| Q25.7 | Other congenital malformations of pulmonary artery | Header |
| Q25.71 | Coarctation of pulmonary artery | Billable |
| Q25.72 | Congenital pulmonary arteriovenous malformation | Billable |
| Q25.79 | Other congenital malformations of pulmonary artery | Billable |
| Q25.8 | Other congenital malformations of other great arteries | Billable |
| Q25.9 | Congenital malformation of great arteries, unspecified | Billable |
Q26
Congenital malformations of great veins
9 subcodes
| Q26.0 | Congenital stenosis of vena cava | Billable |
| Q26.1 | Persistent left superior vena cava | Billable |
| Q26.2 | Total anomalous pulmonary venous connection | Billable |
| Q26.3 | Partial anomalous pulmonary venous connection | Billable |
| Q26.4 | Anomalous pulmonary venous connection, unspecified | Billable |
| Q26.5 | Anomalous portal venous connection | Billable |
| Q26.6 | Portal vein-hepatic artery fistula | Billable |
| Q26.8 | Other congenital malformations of great veins | Billable |
| Q26.9 | Congenital malformation of great vein, unspecified | Billable |
Q27
Other congenital malformations of peripheral vascular system
13 subcodes
| Q27.0 | Congenital absence and hypoplasia of umbilical artery | Billable |
| Q27.1 | Congenital renal artery stenosis | Billable |
| Q27.2 | Other congenital malformations of renal artery | Billable |
| Q27.3 | Arteriovenous malformation (peripheral) | Header |
| Q27.30 | Arteriovenous malformation, site unspecified | Billable |
| Q27.31 | Arteriovenous malformation of vessel of upper limb | Billable |
| Q27.32 | Arteriovenous malformation of vessel of lower limb | Billable |
| Q27.33 | Arteriovenous malformation of digestive system vessel | Billable |
| Q27.34 | Arteriovenous malformation of renal vessel | Billable |
| Q27.39 | Arteriovenous malformation, other site | Billable |
| Q27.4 | Congenital phlebectasia | Billable |
| Q27.8 | Other specified congenital malformations of peripheral vascular system | Billable |
| Q27.9 | Congenital malformation of peripheral vascular system, unspecified | Billable |
Q28
Other congenital malformations of circulatory system
6 subcodes
| Q28.0 | Arteriovenous malformation of precerebral vessels | Billable |
| Q28.1 | Other malformations of precerebral vessels | Billable |
| Q28.2 | Arteriovenous malformation of cerebral vessels | Billable |
| Q28.3 | Other malformations of cerebral vessels | Billable |
| Q28.8 | Other specified congenital malformations of circulatory system | Billable |
| Q28.9 | Congenital malformation of circulatory system, unspecified | Billable |
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Verified against the CMS 2026 code set on May 31, 2026.
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