Other respiratory diseases principally affecting the interstitium
41 codes in this section
About Section J80-J84
Section J80-J84 (J80-J84) covers other respiratory diseases principally affecting the interstitium. It sits within the Diseases of the respiratory system chapter (J00-J99). This section contains 41 ICD-10-CM codes, 31 billable diagnoses you can submit on a claim, and 10 non-billable header codes used to organize the hierarchy.
Codes are organized below by 3-character root. Click the root to see all subcodes underneath it, or click any individual code for full coverage data, payer policies, and linked CPT procedures.
Codes in J80-J84
Grouped by 3-character root code. Click any code for full detail.
| J81.0 | Acute pulmonary edema | Billable |
| J81.1 | Chronic pulmonary edema | Billable |
| J82.8 | Pulmonary eosinophilia, not elsewhere classified | Header |
| J82.81 | Chronic eosinophilic pneumonia | Billable |
| J82.82 | Acute eosinophilic pneumonia | Billable |
| J82.83 | Eosinophilic asthma | Billable |
| J82.89 | Other pulmonary eosinophilia, not elsewhere classified | Billable |
| J84.0 | Alveolar and parieto-alveolar conditions | Header |
| J84.01 | Alveolar proteinosis | Billable |
| J84.02 | Pulmonary alveolar microlithiasis | Billable |
| J84.03 | Idiopathic pulmonary hemosiderosis | Billable |
| J84.09 | Other alveolar and parieto-alveolar conditions | Billable |
| J84.1 | Other interstitial pulmonary diseases with fibrosis | Header |
| J84.10 | Pulmonary fibrosis, unspecified | Billable |
| J84.11 | Idiopathic interstitial pneumonia | Header |
| J84.111 | Idiopathic interstitial pneumonia, not otherwise specified | Billable |
| J84.112 | Idiopathic pulmonary fibrosis | Billable |
| J84.113 | Idiopathic non-specific interstitial pneumonitis | Billable |
| J84.114 | Acute interstitial pneumonitis | Billable |
| J84.115 | Respiratory bronchiolitis interstitial lung disease | Billable |
| J84.116 | Cryptogenic organizing pneumonia | Billable |
| J84.117 | Desquamative interstitial pneumonia | Billable |
| J84.17 | Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere | Header |
| J84.170 | Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere | Billable |
| J84.178 | Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere | Billable |
| J84.2 | Lymphoid interstitial pneumonia | Billable |
| J84.8 | Other specified interstitial pulmonary diseases | Header |
| J84.81 | Lymphangioleiomyomatosis | Billable |
| J84.82 | Adult pulmonary Langerhans cell histiocytosis | Billable |
| J84.83 | Surfactant mutations of the lung | Billable |
| J84.84 | Other interstitial lung diseases of childhood | Header |
| J84.841 | Neuroendocrine cell hyperplasia of infancy | Billable |
| J84.842 | Pulmonary interstitial glycogenosis | Billable |
| J84.843 | Alveolar capillary dysplasia with vein misalignment | Billable |
| J84.848 | Other interstitial lung diseases of childhood | Billable |
| J84.89 | Other specified interstitial pulmonary diseases | Billable |
| J84.9 | Interstitial pulmonary disease, unspecified | Billable |
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Reviewed by the PayerReady Medical Coding Team
Verified against the CMS 2026 code set on May 31, 2026.
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