ICD-10-CM 2026 · Effective October 1, 2025

ICD-10 G40.42

Billable / Specific HCC v28: 79

Cyclin-Dependent Kinase-Like 5 Deficiency Disorder

G40
Block
1
Synonyms
220
LCDs
10
Payer Policies
18
Linked CPTs

About ICD-10-CM G40.42

ICD-10-CM code G40.42 represents Cyclin-Dependent Kinase-Like 5 Deficiency Disorder. This is a billable/specific code in the Nervous System chapter (block G40). The 2026 edition of ICD-10-CM G40.42 became effective on October 1, 2025.

Coding Tips for G40.42

Specialist guidance from the PayerReady Medical Coding Team. Specificity warnings, HCC capture rules, sequencing notes.

HCC capture: document with MEAT each year

G40.42 is a CMS-HCC v28 risk-adjustment code (category 79). To count for the patient Risk Adjustment Factor (RAF), document the diagnosis with MEAT language each calendar year: Monitored, Evaluated, Assessed, Treated. A diagnosis on the problem list alone does not satisfy CMS RADV audit standards. Include the diagnosis in the assessment with current status and current treatment plan.

Inclusion Terms / Approximate Synonyms

Clinical terms and conditions classified under G40.42. Per CMS ICD-10-CM Tabular 2026.

  • CDKL5

Use Additional Code

When coding G40.42, also report these additional codes when applicable.

  • code, if known, to identify associated manifestations, such as:
  • cortical blindness (H47.61-)
  • global developmental delay (F88)

Medicare Advantage HCC Impact

CMS-HCC v28 (current)
Category 79
ESRD-HCC
Category 79
RxHCC (Part D)
Category 79

Capture this diagnosis annually for accurate risk adjustment. Missed HCC captures are the #1 revenue leak in Medicare Advantage risk programs.

Medicare LCD Coverage for G40.42

Local Coverage Determinations (LCDs) from CMS MACs that list G40.42 as a covered diagnosis.

220 LCDs

Showing top 10 of 220 total . Click a CPT for full coverage scope.

CMS LCD: Billing and Coding: Psychological and Neuropsychological Tests
Article ID: 57780, Effective: 2025-10-01 00:00:00, 1784 covered, 1 non-covered
CPT 96131 →
CMS LCD: Billing and Coding: Psychological and Neuropsychological Tests
Article ID: 57780, Effective: 2025-10-01 00:00:00, 1784 covered, 1 non-covered
CPT 96130 →
CMS LCD: Billing and Coding: Psychological and Neuropsychological Tests
Article ID: 57780, Effective: 2025-10-01 00:00:00, 1784 covered, 1 non-covered
CPT 96132 →
CMS LCD: Billing and Coding: Psychological and Neuropsychological Tests
Article ID: 57780, Effective: 2025-10-01 00:00:00, 1784 covered, 1 non-covered
CPT 96133 →
CMS LCD: Billing and Coding: Psychological and Neuropsychological Tests
Article ID: 57780, Effective: 2025-10-01 00:00:00, 1784 covered, 1 non-covered
CPT 96137 →
CMS LCD: Billing and Coding: Psychological and Neuropsychological Tests
Article ID: 57780, Effective: 2025-10-01 00:00:00, 1784 covered, 1 non-covered
CPT 96136 →
CMS LCD: Billing and Coding: Psychological and Neuropsychological Tests
Article ID: 57780, Effective: 2025-10-01 00:00:00, 1784 covered, 1 non-covered
CPT 96139 →
CMS LCD: Billing and Coding: Psychological and Neuropsychological Tests
Article ID: 57780, Effective: 2025-10-01 00:00:00, 1784 covered, 1 non-covered
CPT 96138 →
CMS LCD: Billing and Coding: Psychological and Neuropsychological Tests
Article ID: 57780, Effective: 2025-10-01 00:00:00, 1784 covered, 1 non-covered
CPT G0451 →
CMS LCD: Billing and Coding: Visual Fields Testing
Article ID: 56551, Effective: 2025-10-01 00:00:00, 1427 covered, 0 non-covered
CPT 92082 →

Commercial Payer Coverage

Coverage policies from major commercial payers referencing G40.42.

10 policies

5 Medicare

Billing and Coding: Visual Fields Testing
Policy ID: ART-56551
Billing and Coding: CT of the Head
Policy ID: ART-56612
Billing and Coding: Nerve Conduction Studies and Electromyography
Policy ID: ART-56619
Billing and Coding: Visual Fields Testing
Policy ID: ART-56799
Billing and Coding: Outpatient Speech Language Pathology
Policy ID: ART-56868

CPT Codes Commonly Billed with G40.42

Procedures frequently paired with this diagnosis based on PayerReady's Dx↔Px linkage data.

18 linkages
  • 95711 CMS LCD: Billing and Coding: EEG � Ambulatory Monitoring CMS LCD
  • 95714 CMS LCD: Billing and Coding: EEG � Ambulatory Monitoring CMS LCD
  • 95726 CMS LCD: Billing and Coding: EEG � Ambulatory Monitoring CMS LCD
  • 95709 CMS LCD: Billing and Coding: EEG � Ambulatory Monitoring CMS LCD
  • 95723 CMS LCD: Billing and Coding: EEG � Ambulatory Monitoring CMS LCD
  • 95710 CMS LCD: Billing and Coding: EEG � Ambulatory Monitoring CMS LCD
  • 95716 CMS LCD: Billing and Coding: EEG � Ambulatory Monitoring CMS LCD
  • 95707 CMS LCD: Billing and Coding: EEG � Ambulatory Monitoring CMS LCD
  • 95712 CMS LCD: Billing and Coding: EEG � Ambulatory Monitoring CMS LCD
  • 95724 CMS LCD: Billing and Coding: EEG � Ambulatory Monitoring CMS LCD

Codes Adjacent To G40.42

Other codes in section G40-G47 (Episodic and paroxysmal disorders).

G40 Epilepsy and recurrent seizures (non-billable) G40.0 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset (non-billable) G40.00 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, not intractable (non-billable) G40.001 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, not intractable, with status epilepticus G40.009 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, not intractable, without status epilepticus G40.01 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, intractable (non-billable) G40.011 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, intractable, with status epilepticus G40.019 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, intractable, without status epilepticus G40.1 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures (non-billable) G40.10 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, not intractable (non-billable) G40.101 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, not intractable, with status epilepticus G40.109 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, not intractable, without status epilepticus G40.11 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, intractable (non-billable) G40.111 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, intractable, with status epilepticus G40.119 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, intractable, without status epilepticus G40.2 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures (non-billable) G40.20 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, not intractable (non-billable) G40.201 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, not intractable, with status epilepticus G40.209 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, not intractable, without status epilepticus G40.21 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, intractable (non-billable)

ICD-10 G40.42, Billing FAQ

Is ICD-10 code G40.42 billable? +

Yes, G40.42 is a billable ICD-10-CM code that can appear as a primary or secondary diagnosis on claims.

What other names or terms map to G40.42? +

ICD-10 G40.42 includes: CDKL5.

Does G40.42 affect Medicare Advantage HCC risk adjustment? +

Yes. G40.42 maps to CMS-HCC v28 category 79. Capture this diagnosis annually for accurate Medicare Advantage risk score.

What CPT codes are commonly billed with G40.42? +

Procedures frequently paired with G40.42 include: 95711, 95714, 95726, 95709, 95723.

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Reviewed by the PayerReady Medical Coding Team

Verified against the CMS 2026 code set on June 1, 2026.

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