ICD-10 D47.01
Billable / Specific CCCutaneous mastocytosis
About ICD-10-CM D47.01
ICD-10-CM code D47.01 represents Cutaneous mastocytosis. This is a billable/specific code in the Neoplasms chapter (block D47). The 2026 edition of ICD-10-CM D47.01 became effective on October 1, 2025.
Coding Tips for D47.01
Specialist guidance from the PayerReady Medical Coding Team. Specificity warnings, HCC capture rules, sequencing notes.
D47.01 is designated CC for MS-DRG grouping. On inpatient claims, this code can shift the DRG to the with-CC variant when documented as a present-on-admission secondary diagnosis. Hospital CDI programs flag CC opportunities during chart review. Failure to capture this code may leave 30 to 80 percent of the inpatient stay revenue unrealized.
Inclusion Terms / Approximate Synonyms
Clinical terms and conditions classified under D47.01. Per CMS ICD-10-CM Tabular 2026.
- Diffuse cutaneous mastocytosis
- Maculopapular cutaneous mastocytosis
- Solitary mastocytoma
- Telangiectasia macularis eruptiva perstans
- Urticaria pigmentosa
Type 1 Excludes
Pure excludes, these codes can never be coded together with D47.01. The conditions are mutually exclusive (e.g., congenital vs acquired forms).
- congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
- congenital urticaria pigmentosa (Q82.2)
- extracutaneous mastocytoma (D47.09)
Inpatient DRG Impact, CC
codes Cutaneous mastocytosis. As a Complication/Comorbidity (CC), this contributes to DRG severity adjustment when documented alongside the principal diagnosis.
Medicare LCD Coverage for D47.01
Local Coverage Determinations (LCDs) from CMS MACs that list D47.01 as a covered diagnosis.
Showing top 10 of 1,125 total . Click a CPT for full coverage scope.
Commercial Payer Coverage
Coverage policies from major commercial payers referencing D47.01.
1 Aetna
1 Cigna
5 Medicare
CPT Codes Commonly Billed with D47.01
Procedures frequently paired with this diagnosis based on PayerReady's Dx↔Px linkage data.
We don't have CPT pairings indexed for this specific code yet. Use the CPT search above to find common procedures, or check your payer's published medical policy for code-specific guidance.
Codes Adjacent To D47.01
Other codes in section D37-D48 (Neoplasms of uncertain behavior, polycythemia vera and myelodysplastic syndromes).
ICD-10 D47.01, Billing FAQ
Is ICD-10 code D47.01 billable? +
Yes, D47.01 is a billable ICD-10-CM code that can appear as a primary or secondary diagnosis on claims.
What other names or terms map to D47.01? +
ICD-10 D47.01 includes: Diffuse cutaneous mastocytosis; Maculopapular cutaneous mastocytosis; Solitary mastocytoma, and 2 more clinical synonyms.
What codes are Type 1 Excludes for D47.01? +
Type 1 Excludes (never code together with D47.01): congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2); congenital urticaria pigmentosa (Q82.2); extracutaneous mastocytoma (D47.09)
Is D47.01 a CC or MCC for inpatient DRG? +
Yes, this code is designated as CC. Documenting as a secondary diagnosis on inpatient claims can shift the DRG to a higher-weighted category.
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Reviewed by the PayerReady Medical Coding Team
Verified against the CMS 2026 code set on May 31, 2026.
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